LOCUS       X14608                  2423 bp    mRNA    linear   HUM 18-APR-2005
DEFINITION  Human mRNA for propionyl-CoA carboxylase alpha-chain (EC 6.4.1.3).
ACCESSION   X14608
VERSION     X14608.1
KEYWORDS    propionyl-CoA carboxylase; propionyl-CoA carboxylase alpha.
SOURCE      Homo sapiens (human)
  ORGANISM  Homo sapiens
            Eukaryota; Metazoa; Chordata; Craniata; Vertebrata; Euteleostomi;
            Mammalia; Eutheria; Euarchontoglires; Primates; Haplorrhini;
            Catarrhini; Hominidae; Homo.
REFERENCE   1
  AUTHORS   Lamhonwah A.M.
  JOURNAL   Submitted (08-MAR-1989) to the INSDC. Lamhonwah A.-M.,
            University-Montreal Children's Hospital Research Institute, 2300
            Tupper Street, Montreal, Quebec, Canada H3H 1P3
  REMARK    revised by [3]
REFERENCE   2
  AUTHORS   Lamhonwah A.M., Mahuran D.J., Gravel R.A.
  TITLE     Human mitochondrial propionyl-CoA carboxylase: localization of the
            N-terminus of the pro- and mature alpha chains in the deduced
            primary sequence of a full-length cDNA
  JOURNAL   Nucleic Acids Res. 17(11), 4396-4396(1989).
   PUBMED   2740237
REFERENCE   3  (bases 1 to 2423)
  AUTHORS   Gravel R.
  JOURNAL   Submitted (15-APR-1993) to the INSDC. Gravel R., Hospital For Sick
            Children, 555 University Avenue, Toronto Ontario , CANADA  M5G
            1X8.
FEATURES             Location/Qualifiers
     source          1..2423
                     /db_xref="H-InvDB:HIT000321436"
                     /organism="Homo sapiens"
                     /chromosome="13."
                     /mol_type="mRNA"
                     /clone="pHA32"
                     /db_xref="taxon:9606"
     misc_feature    1..26
                     /note="mitochondrial leader peptide"
     sig_peptide     49..108
     CDS             49..2160
                     /gene="PCCA"
                     /standard_name="propionyl-CoA carboxylase alpha-chain"
                     /product="propionyl-CoA carboxylase"
                     /EC_number="6.4.1.3"
                     /db_xref="GOA:P05165"
                     /db_xref="H-InvDB:HIT000321436.13"
                     /db_xref="HGNC:HGNC:8653"
                     /db_xref="InterPro:IPR000089"
                     /db_xref="InterPro:IPR001882"
                     /db_xref="InterPro:IPR005479"
                     /db_xref="InterPro:IPR005481"
                     /db_xref="InterPro:IPR005482"
                     /db_xref="InterPro:IPR011053"
                     /db_xref="InterPro:IPR011054"
                     /db_xref="InterPro:IPR011761"
                     /db_xref="InterPro:IPR011764"
                     /db_xref="InterPro:IPR016185"
                     /db_xref="InterPro:IPR041265"
                     /db_xref="PDB:2CQY"
                     /db_xref="PDB:2JKU"
                     /db_xref="UniProtKB/Swiss-Prot:P05165"
                     /protein_id="CAA32763.1"
                     /translation="MLSAALRTLKHVLYYSRQCLMVSRNLGSVGYDPNEKTFDKILVA
                     NRGEIACRVIRTCKKMGIKTVAIHSDVDASSVHVKMADEAVCVGPAPTSKSYLNMDAI
                     MEAIKKTRAQAVHPGYGFLSENKEFARCLAAEDVVFIGPDTHAIQAMGDKIESKLLAK
                     KAEVNTIPGFDGVVKDAEEAVRIAREIGYPVMIKASAGGGGKGMRIAWDDEETRDGFR
                     LSSQEAASSFGDDRLLIEKFIDNPRHIEIQVLGDKHGNALWLNERECSIQRRNQKVVE
                     EAPSIFLDAETRRAMGEQAVALARAVKYSSAGTVEFLVDSKKNFYFLEMNTRLQVEHP
                     VTECITGLDLVQEMIRVAKGYPLRHKQADIRINGWAVECRVYAEDPYKSFGLPSIGRL
                     SQYQEPLHLPGVRVDSGIQPGSDISIYYDPMISKLITYGSDRTEALKRMADALDNYVI
                     RGVTHNIALLREVIINSRFVKGDISTKFLSDVYPDGFKGHMLTKSEKNQLLAIASSLF
                     VAFQLRAQHFQENSRMPVIKPDIANWELSVKLHDKVHTVVASNNGSVFSVEVDGSKLN
                     VTSTWNLASPLLSVSVDGTQRTVQCLSREAGGNMSIQFLGTVYKVNILTRLAAELNKF
                     MLEKVTEDTSSVLRSPMPGVVVAVSVKPGDAVAEGQEICVIEAMKMQNSMTAGKTGTV
                     KSVHCQAGDTVGEGDLLVELE"
     mat_peptide     109..2157
                     /gene="PCCA"
                     /standard_name="propionyl-CoA carboxylase alpha-chain"
                     /product="propionyl-CoA carboxylase"
                     /EC_number="6.4.1.3"
     misc_feature    340..366
                     /note="conflicts with paper 1989"
     misc_feature    1066..1146
                     /note="conflicts with paper 1989"
     regulatory      2386..2391
                     /regulatory_class="polyA_signal_sequence"
BASE COUNT          713 a          470 c          597 g          643 t
ORIGIN      
        1 cccgctggtc gctgccggac ggcgtgggcg gtggccgcgc agcagctgat gctgagcgcg
       61 gcgctgcgga ccctgaagca tgttctgtac tattcaagac agtgcttaat ggtgtcccgt
      121 aatcttggtt cagtgggata tgatcctaat gaaaaaactt ttgataaaat tcttgttgct
      181 aatagaggag aaattgcatg tcgggttatt agaacttgca agaagatggg cattaagaca
      241 gttgccatcc acagtgatgt tgatgctagt tctgttcatg tgaaaatggc ggatgaggct
      301 gtctgtgttg gcccagctcc caccagtaaa agctacctca acatggatgc catcatggaa
      361 gccattaaga aaaccagggc ccaagctgta catccaggtt atggattcct ttcagaaaac
      421 aaagaatttg ccagatgttt ggcagcagaa gatgtcgttt tcattggacc tgacacacat
      481 gctattcaag ccatgggcga caagattgaa agcaaattat tagctaagaa agcagaggtt
      541 aatacaatcc ctggctttga tggagtagtc aaggatgcag aagaagctgt cagaattgca
      601 agggaaattg gctaccctgt catgatcaag gcctcagcag gtggtggtgg gaaaggcatg
      661 cgcattgctt gggatgatga agagaccagg gatggtttta gattgtcatc tcaagaagct
      721 gcttctagtt ttggcgatga tagactacta atagaaaaat ttattgataa tcctcgtcat
      781 atagaaatcc aggttctagg tgataaacat gggaatgctt tatggcttaa tgaaagagag
      841 tgctcaattc agagaagaaa tcagaaggtg gtggaggaag caccaagcat ttttttggat
      901 gcggagactc gaagagcgat gggagaacaa gctgtagctc ttgccagagc agtaaaatat
      961 tcctctgctg ggaccgtgga gttccttgtg gactctaaga agaattttta tttcttggaa
     1021 atgaatacaa gactccaggt tgagcatcct gtcacagaat gcattactgg cctggaccta
     1081 gtccaggaaa tgatccgtgt tgctaagggc taccctctca ggcacaaaca agctgatatt
     1141 cgcatcaacg gctgggcagt tgaatgtcgg gtttatgctg aggaccccta caagtctttt
     1201 ggtttaccat ctattgggag attgtctcag taccaagaac cgttacatct acctggtgtc
     1261 cgagtggaca gtggcatcca accaggaagt gatattagca tttattatga tcctatgatt
     1321 tcaaaactaa tcacatatgg ctctgataga actgaggcac tgaagagaat ggcagatgca
     1381 ctggataact atgttattcg aggtgttaca cataatattg cattacttcg agaggtgata
     1441 atcaactcac gctttgtaaa aggagacatc agcactaaat ttctctccga tgtgtatcct
     1501 gatggcttca aaggacacat gctaaccaag agtgagaaga accagttatt ggcaatagca
     1561 tcatcattgt ttgtggcatt ccagttaaga gcacaacatt ttcaagaaaa ttcaagaatg
     1621 cctgttatta aaccagacat agccaactgg gagctctcag taaaattgca tgataaagtt
     1681 cataccgtag tagcatcaaa caatgggtca gtgttctcgg tggaagttga tgggtcgaaa
     1741 ctaaatgtga ccagcacgtg gaacctggct tcgcccttat tgtctgtcag cgttgatggc
     1801 actcagagga ctgtccagtg tctttctcga gaagcaggtg gaaacatgag cattcagttt
     1861 cttggtacag tgtacaaggt gaatatctta accagacttg ccgcagaatt gaacaaattt
     1921 atgctggaaa aagtgactga ggacacaagc agtgttctgc gttccccgat gcccggagtg
     1981 gtggtggccg tctctgtcaa gcctggagac gcggtagcag aaggtcaaga aatttgtgtg
     2041 attgaagcca tgaaaatgca gaatagtatg acagctggga aaactggcac ggtgaaatct
     2101 gtgcactgtc aagctggaga cacagttgga gaaggggatc tgctcgtgga gctggaatga
     2161 aggatttata acctttcagt catcacccaa tttaattagc catttgcatg atgctttcac
     2221 acacaattga ttcaagcatt atacaggaac acccctgtgc agctacgttt acgtcgtcat
     2281 ttattccaca gagtcaagac caatattctg ccaaaaaatc accaatggaa attttcatga
     2341 tataaatact tgtactatag atgtacttct gctgtgagat tccctagtgt caaaattaaa
     2401 tcaataaaac tgagcatttg tct
//