LOCUS       HUMICOA                 1881 bp    mRNA    linear   HUM 08-NOV-1994
DEFINITION  Human isovaleryl-coA dehydrogenase (IVD) mRNA, complete cds.
ACCESSION   M34192
VERSION     M34192.1
KEYWORDS    isovaleryl-CoA dehydrogenase.
SOURCE      Homo sapiens (human)
  ORGANISM  Homo sapiens
            Eukaryota; Metazoa; Chordata; Craniata; Vertebrata; Euteleostomi;
            Mammalia; Eutheria; Euarchontoglires; Primates; Haplorrhini;
            Catarrhini; Hominidae; Homo.
REFERENCE   1  (bases 1 to 1881)
  AUTHORS   Matsubara,Y., Ito,M., Glassberg,R., Satyabhama,S., Ikeda,Y. and
            Tanaka,K.
  TITLE     Nucleotide sequence of messenger RNA encoding human
            isovaleryl-coenzyme A dehydrogenase and its expression in
            isovaleric acidemia fibroblasts
  JOURNAL   J. Clin. Invest. 85 (4), 1058-1064 (1990)
   PUBMED   2318964
COMMENT     Original source text: Human placenta, cDNA to mRNA, (library of
            Clontech).
FEATURES             Location/Qualifiers
     source          1..1881
                     /db_xref="H-InvDB:HIT000195572"
                     /organism="Homo sapiens"
                     /mol_type="mRNA"
                     /db_xref="taxon:9606"
                     /map="15q14-q15"
     gene            1..1881
                     /gene="IVD"
     mRNA            <1..1881
                     /gene="IVD"
                     /note="isovaleryl-coA dehydrogenase mRNA; G00-119-354"
     CDS             16..1287
                     /gene="IVD"
                     /note="isovaleryl-coA dehydrogenase (IVD)"
                     /codon_start=1
                     /protein_id="AAA52711.1"
                     /db_xref="GDB:G00-119-354"
                     /translation="MATATRLLGWRVASWRLRPPLAGFVSQRAHSLLPVDDAINGLSE
                     EQRQLRQTMAKFLQEHLAPKAQEIDRSNEFKNLREFWKQLGNLGVLGITAPVQYGGSG
                     LGYLEHVLVMEEISRASGAVGLSYGAHSNLCINQLVRNGNEAQKEKYLPKLISGEYIG
                     ALAMSEPNAGSDVVSMKLKAEKKGNHYILNGNKFWITNGPDADVLIVYAKTDLAAVPA
                     SRGITAFIVEKGMPGFSTSKKLDKLGMRGSNTCELIFEDCKIPAANILGHENKGVYVL
                     MSGLDLERLVLAGGPLGLMQAVLDHTIPYLHVREAFGQKIGHFQLMQGKMADMYTRLM
                     ACRQYVYNVAKACDEGHCTAKDCAGVILYSAECATQVALDGIQCFGGNGYINDFPMGR
                     FLRDAKLYEIGAGTSEVRRLVIGRAFNADFH"
BASE COUNT          396 a          497 c          554 g          434 t
ORIGIN      
        1 tcgtgcatgg cagagatggc gactgcgact cggctgctgg ggtggcgtgt ggcgagctgg
       61 aggctgcggc cgccgcttgc cggcttcgtt tcccagcggg cccactcgct tttgcccgtg
      121 gacgatgcaa tcaatgggct aagcgaggag cagaggcagc ttcgtcagac catggctaag
      181 ttccttcagg agcacctggc ccccaaggcc caggagatcg atcgcagcaa tgagttcaag
      241 aacctgcgag aattttggaa gcagctgggg aacctgggcg tattgggcat cacagcccct
      301 gttcagtatg gcggctccgg cctgggctac ctggagcatg tgctggtgat ggaggagata
      361 tcccgagctt ccggagcagt ggggctcagt tacggtgccc actccaacct ctgcatcaac
      421 cagcttgtac gcaatgggaa tgaggcccag aaagagaagt atctcccgaa gctgatcagt
      481 ggtgagtaca tcggagccct ggccatgagt gagcccaatg caggctctga tgttgtctct
      541 atgaagctca aagcggaaaa gaaaggaaat cactacatcc tgaatggcaa caagttctgg
      601 atcactaatg gccctgatgc tgacgtcctg attgtctatg ccaagacaga tctggctgct
      661 gtgccagctt ctcggggcat cacagccttc attgtggaga agggtatgcc tggctttagc
      721 acctctaaga agctggacaa gctggggatg aggggctcta acacctgtga gctaatcttt
      781 gaagactgca agattcctgc tgccaacatc ctgggccatg agaataaggg tgtctacgtg
      841 ctgatgagtg ggctggacct ggagcggctg gtgctggccg gggggcctct tgggctcatg
      901 caagcggtcc tggaccacac cattccctac ctgcacgtga gggaagcctt tggccagaag
      961 atcggccact tccagttgat gcaggggaag atggctgaca tgtacacccg cctcatggcg
     1021 tgtcggcagt atgtctacaa tgtcgccaag gcctgcgatg agggccattg cactgctaag
     1081 gactgtgcag gtgtgattct ttactcagct gagtgtgcta cacaggtagc cctggacggc
     1141 attcagtgtt ttggtggcaa tggctacatc aatgactttc ccatgggccg ctttcttcga
     1201 gatgccaagc tgtatgagat aggggctggg accagcgagg tgaggcggct ggtcatcggc
     1261 agagccttca atgcagactt tcactagtcc tgagaccctt cgcccccttt tcctgcacct
     1321 agtggccttt cttgggaagt agagatgtgg cggctttccc accctgccca cagcaggccc
     1381 tcctgcccag ctgctcttgt cagccctctg gcctctggat gaggttgagt tctccacaac
     1441 agctcccaag catcatgggc ctcgcagccg ggcctgtgcc acggctagtg ttgtgtgatt
     1501 taaaatggac tcagcaggaa gcatattgtc tggggattgt tgggacaggt tttggtgact
     1561 ctgtgccctt gctctctaac ttctgagccc acctcccagg gtaggcacct gggggcatgc
     1621 aggtgcccac ctcccagggt aggcacctgg gggcatgcag gtacccacct ctttctcttg
     1681 ggtgaggctc tggcaaggag atctctctgc tcaagcacag cagaatcatg gcccctctcc
     1741 atgaattgga acttggtaca ggttaagtat ccctaatcct gaaatctgaa acacttgtgg
     1801 ttccaagcat tttggataag gcaaattcaa ctttcagtct cttttctggg ggaaaaaaat
     1861 aataaaccta gcctagccag g
//